Fundus changes in incontinentia pigmenti (Bloch-Sulzberger syndrome).
نویسندگان
چکیده
A case of incontinentia pigmenti is reported with fundus changes in 1 eye. She had microaneurysms temporal to the macula, with an abnormal branch of inferior temporal vein. There was extensive retinitis proliferans in the upper temporal equatorial region, which showed leakage on fluorescein angiography.
منابع مشابه
Fundus changes in incontinentia pigmenti ( Bloch - Sulzberger syndrome ) : a case report
The ocular and systemic changes in incontinentia pigmenti are reviewed here and a case is reported with fundus changes which have not been described previously. Incontinentia pigmenti (IP) is characterised by ectodermal defects, with occasional associated mesodermal abnormalities. The typical skin lesions are blue-grey to chocolate-brown arranged along the naevus lines of Blaschko. These occur ...
متن کاملIncontinentia pigmenti (Bloch-Sulzberger syndrome) and retinal changes.
Incontinentia pigmenti is associated with various anomalies in 80% of cases. Among the most important are the ocular abnormalities and more particularly a retrolental mass with detachment of a dysplastic retina. At the basis of this manifestation are retinal vascular changes, characterised at first by ectatic tortuous veins and arteriovenous anastomoses as well as by aneurysmal-like dilatations.
متن کاملOcular changes in the Bloch-Sulzberger syndrome (Incontinentia pigmenti)
THE Bloch-Sulzberger syndrome is a familial condition consisting chiefly of ectodermal defects, of which changes in the skin, nails, hair, teeth, central nervous system, and eyes are the most common. The final dermal phase "incontinentia pigmenti" has received the most attention. This disease can be described as a rare and peculiar abnormality of development found almost exclusively in females ...
متن کاملگزارش یک مورد Incontinentia pigmenti
سابقه و هدف: (IP) Incontinentia pigmenti یا سندرم Bloch-Sulzberger اولین بار توسط Garrod در سال 1906 معرفی گردید. سپس، در سال 1926 توسط Bloch و در سال 1927 توسط Sulzberger گزارش شد. این بیماری یک بیماری ژنتیکی پوستی است که از نظر توارث وابسته به جنس غالب می باشد. ماکول های نامنظم، شیر قهوه ای یا خاکستری یا ضایعات آتروفیک، فرورفته و دپیگمانته از علایم پوستی این بیماری می باشند. هدف مقاله حاضر مع...
متن کامل[Incontinentia pigmenti (the Bloch-Sulzberger syndrome)].
The course and histologic skin signs are described at the stage of inflammation in 2 cases of incontinentia pigmenti (IP) or the Bloch-Sulzberger syndrome. In the authors' opinion, the pigmentary stage of skin lesion in IP does not replace the warty stage, but accompanies it or the inflammatory one as blebs disappear. In IP, the latter contain eosinophils; there is plasma and cell infiltration ...
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ورودعنوان ژورنال:
- American journal of ophthalmology
دوره 45 2 شماره
صفحات -
تاریخ انتشار 1958